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Ivo Barić Selected Research
Ivo Barić Research Topics
Disease
4
Muscular Diseases (Myopathy)
01/2022 - 08/2013
4
Hypermethioninemia
01/2021 - 11/2012
3
Wolman Disease (Wolman's Disease)
01/2022 - 03/2015
3
Hyperammonemia
03/2021 - 09/2016
3
Homocystinuria
01/2021 - 03/2011
3
Inborn Urea Cycle Disorders
01/2021 - 03/2019
3
Mitochondrial Diseases (Mitochondrial Disease)
01/2021 - 08/2013
3
Cardiomyopathies (Cardiomyopathy)
01/2018 - 11/2015
3
Muscle Hypotonia (Hypotonia)
01/2018 - 11/2003
3
Seizures (Absence Seizure)
01/2018 - 09/2016
2
MELAS Syndrome (Syndrome, MELAS)
01/2021 - 05/2008
2
Inborn Errors Metabolism (Inborn Errors of Metabolism)
01/2021 - 08/2007
2
Propionic Acidemia
01/2021 - 11/2015
2
Methylenetetrahydrofolate reductase deficiency
01/2021 - 01/2019
2
Phenylketonurias (Phenylketonuria)
01/2021 - 07/2009
2
Liver Failure
01/2020 - 03/2015
2
Brain Diseases (Brain Disorder)
03/2019 - 05/2008
2
Hypoglycemia (Reactive Hypoglycemia)
01/2018 - 09/2016
2
Ornithine Carbamoyltransferase Deficiency Disease
03/2016 - 11/2015
2
Megalencephaly
11/2015 - 11/2003
2
Fibrosis (Cirrhosis)
09/2015 - 03/2015
1
Neurologic Manifestations (Neurological Manifestations)
05/2021
1
Gaucher Disease (Gaucher's Disease)
05/2021
1
Acute Intermittent Porphyria (Porphyria, Acute)
01/2021
1
Mucopolysaccharidosis III (Sanfilippo Syndrome)
01/2021
1
succinic semialdehyde dehydrogenase deficiency
01/2021
1
Type C Niemann-Pick Disease (Niemann Pick Disease, Type C)
01/2021
1
Autism Spectrum Disorder
01/2021
1
Cerebrotendinous Xanthomatosis
01/2021
1
Smith-Lemli-Opitz Syndrome
01/2021
1
Hartnup Disease
01/2021
1
Hepatolenticular Degeneration (Wilson's Disease)
01/2021
1
Lesch-Nyhan Syndrome (Choreoathetosis Self Mutilation Hyperuricemia Syndrome)
01/2021
1
Neuronal Ceroid-Lipofuscinoses (Neuronal Ceroid Lipofuscinosis)
01/2021
1
Optic Atrophy
01/2020
1
Pelger-Huet Anomaly
01/2020
1
Tyrosinemias (Tyrosinemia)
04/2019
1
Free sialic acid storage disease
10/2018
1
Agammaglobulinemia (Hypogammaglobulinemia)
10/2018
1
Gyrate Atrophy
10/2018
1
Galactosemias (Galactosemia)
01/2018
1
Hyperphosphatasia with Mental Retardation
01/2018
1
Attention Deficit Disorder with Hyperactivity (Attention Deficit Hyperactivity Disorder)
01/2018
1
Hypertrophic Cardiomyopathy (Hypertrophic Obstructive Cardiomyopathy)
01/2018
1
Sialorrhea
12/2017
1
Canavan Disease (Leukodystrophy, Spongiform)
01/2017
1
Hepatomegaly
01/2017
1
Cognitive Dysfunction
09/2016
Drug/Important Bio-Agent (IBA)
6
Proteins (Proteins, Gene)
FDA Link
01/2020 - 03/2011
5
Enzymes
IBA
10/2018 - 05/2008
4
Amino Acids
FDA Link
01/2021 - 03/2011
3
Creatine Kinase (Creatine Phosphokinase)
IBA
01/2022 - 08/2013
3
Acids
IBA
01/2021 - 11/2003
3
Ligases (Synthetase)
IBA
11/2019 - 03/2011
2
Sebelipase alfa
IBA
01/2022 - 09/2015
2
Adenosine Triphosphate (ATP)
IBA
03/2021 - 05/2008
2
Cholesterol
IBA
01/2021 - 06/2012
2
Ornithine Carbamoyltransferase (Ornithine Transcarbamylase)
IBA
11/2019 - 11/2015
2
DNA (Deoxyribonucleic Acid)
IBA
04/2019 - 01/2016
2
Alkaline Phosphatase
IBA
01/2018 - 12/2009
2
Transfer RNA (tRNA)
IBA
01/2018 - 08/2013
2
S-Adenosylhomocysteine
IBA
01/2017 - 12/2010
2
Methionine (L-Methionine)
FDA Link
01/2017 - 12/2010
2
Transaminases (Aminotransferases)
IBA
01/2017 - 12/2010
2
S-Adenosylmethionine (Ademetionine)
IBA
01/2017 - 12/2010
1
Ambroxol (Mucosolvan)
IBA
05/2021
1
purine
IBA
01/2021
1
Adenylosuccinate lyase deficiency
IBA
01/2021
1
Adenylosuccinate Lyase
IBA
01/2021
1
Neurotransmitter Agents (Neurotransmitter)
IBA
01/2021
1
Copper
IBA
01/2021
1
Creatine
IBA
01/2021
1
Folic Acid (Vitamin M)
FDA Link
Generic
01/2021
1
Heme (Haem)
IBA
01/2021
1
Phosphotransferases (Kinase)
IBA
01/2021
1
Iron
IBA
01/2021
1
Oxidoreductases (Dehydrogenase)
IBA
01/2021
1
Arginine (L-Arginine)
FDA Link
11/2019
1
Citrulline
IBA
11/2019
1
HHH syndrome
IBA
11/2019
1
fumarylacetoacetase (fumarylacetoacetate hydrolase)
IBA
04/2019
1
Tyrosine (L-Tyrosine)
FDA Link
04/2019
1
succinylacetone
IBA
04/2019
1
Methionine Adenosyltransferase
IBA
01/2019
1
Immunoglobulin G (IgG)
IBA
10/2018
1
N-Acetylneuraminic Acid (Sialic Acid)
IBA
10/2018
1
Ornithine-Oxo-Acid Transaminase (Ornithine Aminotransferase)
IBA
10/2018
1
Galactose (Galactopyranose)
FDA Link
Generic
01/2018
1
galactose-1-phosphate
IBA
01/2018
1
Lactic Acid (Lactate)
FDA Link
Generic
01/2018
1
Carnitine (L-Carnitine)
FDA Link
Generic
01/2018
1
aspartoacylase
IBA
01/2017
1
Ammonia
IBA
09/2016
Therapy/Procedure
2
Therapeutics
04/2019 - 09/2015
2
Enzyme Replacement Therapy
09/2015 - 03/2015
1
Renal Dialysis (Hemodialysis)
03/2021
1
Induced Hypothermia
03/2019
1
Ketogenic Diet
01/2018
1
Hearing Aids (Hearing Aid)
12/2017
1
Cochlear Implants (Cochlear Implant)
12/2017